September 2019 HSC Section 1 Congenital and Pediatric Problems

Reprinted by permission of Int J Pediatr Otorhinolaryngol. 2016; 90:251-258.

International Journal of Pediatric Otorhinolaryngology 90 (2016) 251 e 258

Contents lists available at ScienceDirect

International Journal of Pediatric Otorhinolaryngology

journal homepage: http://www.ijporlonline.com/

Review Article International Pediatric Otolaryngology Group (IPOG) consensus recommendations: Hearing loss in the pediatric patient Bryan J. Liming a , * , John Carter b , Alan Cheng c , Daniel Choo d , John Curotta c , Daniela Carvalho e , John A. Germiller f , Stephen Hone g , Margaret A. Kenna h , Natalie Loundon i , Diego Preciado j , Anne Schilder k , Brian K. Reilly j , Stephane Roman l , Julie Strychowsky m , Jean-Michel Triglia l , Nancy Young n , Richard J.H. Smith a

a Department of Otolaryngology -Head and Neck Surgery, University of Iowa Health Care, Iowa City, IA, USA b Department of Otolaryngology- Head and Neck Surgery, Ochsner Medical Center, New Orleans, LA, USA

c Sydney Children's Hospital Network, Sydney, Australia d Cincinnati Children's Hospital, Cincinnati, OH, USA e Rady Children's Hospital, San Diego, CA, USA f Children's Hospital of Philadelphia, Philadelphia PA, USA g Our Lady's Children's Hospital, Crumlin, Dublin, Ireland

h Department of Otolaryngology and Communication Enhancement, Boston Children's Hospital, Boston MA, USA i Pediatric ENT Department, Hopital Necker-Enfants Malades, AP-HP Universite Paris Descartes, Paris, France j Department of Otolaryngology, Children's National Hospital, Washington DC, USA k Evident, UCL Ear Institute, Royal National Throat, Nose and Ear Hospital, London UK l Department of Pediatric Otolaryngology, La Timone Children's Hospital, Aix-Marseille Universite ’ , Marseille, France m Paediatric Otolaryngology-Head and Neck Surgery-Children's Hospital at London Health Sciences Centre, London, Ontario, Canada n Division of Otolaryngology-Head and Neck Surgery, Ann & Robert H. Lurie Children's Hospital of Chicago, Chicago IL, USA

a r t i c l e i n f o

a b s t r a c t

Article history: Received 12 September 2016 Accepted 13 September 2016 Available online 15 September 2016 Keywords: Congenital hearing loss Consensus statement Comprehensive genetic testing Sensorineural hearing loss Conductive hearing loss

Objective: To provide recommendations for the workup of hearing loss in the pediatric patient. Methods: Expert opinion by the members of the International Pediatric Otolaryngology Group. Results: Consensus recommendations include initial screening and diagnosis as well as the workup of sensorineural, conductive and mixed hearing loss in children. The consensus statement discusses the role of genetic testing and imaging and provides algorithms to guide the workup of children with hearing loss. Conclusion: The workup of children with hearing loss can be guided by the recommendations provided herein. Published by Elsevier Ireland Ltd.

Contents

1. Consensus objectives . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . 252 2. Target population . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . 252 3. Intended users . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . 252

Abbreviations: aABR, automated brainstem response; ABR, auditory brainstem response; ANSD, auditory neuropathy spectrum disorder; CGT, comprehensive ge- netic testing; CHL, conductive hearing loss; CMV, cytomegalovirus; CT, computed tomography; EAC, external auditory canal; IPOG, International Pediatric Otolaryn- gology Group; MRI, magnetic resonance imaging; OAEs, otoacoustic emissions; SNHL, sensorineural hearing loss. * Corresponding author. Department of Otolaryngology e Head and Neck Sur- gery, University of Iowa Hospitals and Clinics, USA. E-mail address: Bryan-liming@uiowa.edu (B.J. Liming).

http://dx.doi.org/10.1016/j.ijporl.2016.09.016 0165-5876/Published by Elsevier Ireland Ltd.

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