2017 Sec 1 Green Book

Friedmann DR, Ahmed OH, McMenomey SO, et al. Single-sided deafness cochlear implantation: candidacy, evaluation, and outcomes in children and adults. Otol Neurotol . 2016; 37(2):e154-e160. EBM level 4.............................................................................125-131 Summary : This is a r etrospective case series of 16 patients (four children) with unilateral severe-to-profound sensorineural hearing loss who underwent ipsilateral cochlear implantation. The consonant-nucleus-consonant (CNC) and hearing-in-noise test scores were significantly improved from the preoperative condition.

Greinwald J, DeAlarcon A, Cohen A, et al. Significance of unilateral enlarged vestibular aqueduct. Laryngoscope. 2013; 123(6):1537-1546. EBM level 2...............................132-141

Summary : The authors identified 144 children with unilateral and bilateral enlarged vestibular aqueducts (EVA) as well as a comparison group of children with hearing loss but no EVA. They looked at the incidence of ipsilateral and contralateral hearing loss as well as the rate of hearing loss progression. They found that children with unilateral EVA have a significant risk of progression of hearing loss in the ipsilateral and/or contralateral ear, and that they are more likely to progress than children with hearing loss without an EVA on imaging. This is a slightly older paper, but a revolutionary one. Sloan-Heggen CM, Bierer AO, Shearer AE, et al. Comprehensive genetic testing in the clinical evaluation of 1119 patients with hearing loss. Hum Genet . 2016; 135(4):441-450. EBM level 4....................................................................................................................142-151 Summary : This study details the results of samples from 1119 sequential patients referred to the University of Iowa for comprehensive genetic testing for hearing loss. Researchers identified the underlying genetic cause in 39% of samples. The diagnostic rate was highest for patients with autosomal dominant hearing loss, congenital onset, and bilateral symmetric hearing loss. The authors offer an algorithm for workup of patients based on phenotype. Wang MC, Wang YP, Chu CH, et al. The protective effect of adenoidectomy on pediatric tympanostomy tube re-insertions: a population-based birth cohort study. PLOS One . 2014; 9(7):e101175. EBM level 2............................................................................................152-158 Summary : This article analyzed the rate of second set of tympanostomy tube insertion in cohorts of children in that underwent tube insertion alone vs. tube insertion with adenoidectomy. They found that adenoidectomy with the first set of tubes decreased the rate of tube reinsertion, especially for children over the age of 4 years at the time of their first tube surgery.