•
1-2% of all NHL
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7-8% of extranodal lymphomas
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Ocular adnexa lymphomas (OAL) include:
o
orbit
o
extra ocular muscles
o
conjunctiva
o
eyelids
o
lacrimal gland
o
apparatus
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Most cases of extraocular orbital lymphoma are Marginal Zone Lymphoma (MZL)
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Approximately 15% of such cases are bilateral (synchronous or metachronous)
Orbital (ocular adnexal) Lymphoma