•
5
th
- 7
th
decade of life (median age, 65 years)
•
female predominance (male:female = 1:1.5/2)
•
Korean populations: younger age (median, 46 years) at the time of
diagnosis, male rather than female predominance
•
Site of origin:
o
orbit = 40%
o
conjunctiva = 35%-40%
o
lacrimal gland = 10%-15%
o
eyelid = 10%
•
Bilateral involvement in 10% to 15% of cases (80% simultaneous,
20% sequential events)
Clinical presentation