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Epidemiology

• ES is nonetheless an infrequent cancer, with

approximately 250-300 new cases diagnosed in

patients < 20 yrs of age per year in North America

• Incidence is low before age of 5 yrs: 0.6 per million,

but progressively rises towards puberty (peak rate of

5 per million)

• The most common age of diagnosis is the 2

nd

decade

of life (65%)

• Males > Females (1.3 : 1)