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1-2% of all NHL
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7-8% of extranodal lymphomas
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Ocular adnexa lymphomas (OAL) include:
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orbit
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extra ocular muscles
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conjunctiva
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eyelids
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lacrimal gland
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apparatus
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Most cases of extraocular orbital lymphoma are Marginal Zone Lymphoma (MZL)
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Approximately 15% of such cases are bilateral (synchronous or metachronous)
Orbital (ocular adnexal) Lymphoma