![Show Menu](styles/mobile-menu.png)
![Page Background](./../common/page-substrates/page0148.jpg)
sound (CROS) amplification devices or osseointegrated
devices such as bone anchored hearing aids (BAHA).
Although both of these approaches provide the patients
with some access to sound, the configurations do not
restore hearing to the deaf ear but rather route the signals
so that the benefits of binaural hearing are not maximally
achieved as previously demonstrated (5). Even with such
technology, improved hearing in difficult listening situ-
ations and the ability to localize sound remain elusive to
most patients with SSD (6) and may actually make
listening more difficult with certain signal-to-noise ratios
incident on the unaffected ear. Cochlear implants for
SSD were first introduced in the setting of intractable
tinnitus (7), but have since been shown to have benefits
far beyond tinnitus suppression (8,9).
Our purpose in this article was to review our institu-
tional experience with selecting appropriate SSD
pediatric and adult patients to receive a cochlear implant
for various indications and their subjective and objective
outcomes to date to determine if 1) there is a functional
increase in word and sentence recognition in quiet and in
noise and 2) the binaural advantage can be restored by
placing a cochlear implant in the poorer ear.
METHODS
Subjects
This retrospective chart review was approved by our institu-
tional review board (IRB) and included 12 adult patients and 4
children with SSD. All patients had unaidable hearing in the
affected ear. There were no strict hearing criteria in the better
and all patients were evaluated on an individual basis but the
average PTA in the better hearing ear was 12.7 (SD 7.0). All
patients contributing data had at least 1 year of CI use.
See Table 1 for adult demographic factors. Most subjects
were deaf as a result of sudden sensorineural hearing loss
(SSNHL) (67%), and did not have any pathology in their
normal hearing ear (83%). The PTA of the deaf ear among
all subjects was 87.0 (SD 8.3). The mean age at diagnosis
among adult patients with SSDwas 47.3 years (SD 12.4) and on
average they were implanted 3.1 years (SD 5.7) later. Eleven
adult patients received Cochlear Nucleus (Englewood, CO,
U.S.A.) devices and one received Advanced Bionics (Valencia,
CA, U.S.A.) devices. All four children received Cochlear
Nucleus devices. Intraoperatively, all patients had full inser-
tions of the electrode array without perioperative or
postoperative complications.
Speech Perception
Patients were evaluated according to our institutional SSD
protocol (Table 2). Before the availability of direct connect, a
‘‘plug and muff’’ technique was used to minimize/eliminate the
role of better hearing ear (n
¼
4) in a sound-proof booth using
recorded material. To ensure that the poor ear was completely
isolated from the ‘‘good’’ ear on the nonimplanted side, the
good ear was plugged and muffed using E.A.R. foam earplugs
(3M Co., St. Paul, MN, U.S.A.) and TASCO sound shield over-
the-head earmuff Model #2900. (TASCO Corp, Riverside, RI,
U.S.A.). For the plug, the mean attenuation for frequencies 125
to 8000 Hz was 42.3 dB with a noise reduction rating (NRR) of
29. The muff had a mean attenuation of 33.9 dB for frequencies
125 to 8000 Hz with an NRR of 29.
Later in our experience, a manufacturer-specific direct
connect system to the cochlear implant sound processor was
used to allow isolation of the CI ear for testing with an insert
earphone in the unaffected ear. Direct connect (DC) audio-
metric testing (Cochlear Americas), via electrical cable con-
nection, to the cochlear implant processor allows testing of
each ear in isolation or together (binaurally) using tones or
speech. This allows elimination of the inadvertent role of the
better hearing ear in sound field testing and allows for hearing
in noise testing with spatially separated competing signal and
sound localization without the need for multispeaker arrays.
The generalizability of this system has been validated else-
where including precise timing and level cues (10–12). The
signals are processed via a head-related transfer function
(HRTF) so that it is equivalent to sound field presentation
and the software provides calibration to ensure that the signals
are delivered at the desired presentation levels.
TABLE 1.
Demographics
Category
n (%)
Sex
Male
6 (50)
SSD ear
Left
7 (58)
Etiology of SSD
SSNHL
8 (67)
Other
4 (33)
Pathology in normal ear
Yes
2 (17)
Mean (SD)
Age at implantation
50.5 (13.4)
Age at deafness
47.3 (12.4)
Pure-tone average (PTA); 0.5, 1, 2 kHz
Normal ear
12.7 (7.0)
SSD ear
87.0 (8.3)
Duration of deafness to CI (yr)
3.1 (5.7)
Length postoperative follow-up (yr)
3.4 (1.8)
Demographics of adult SSD patients who underwent cochlear
implantation at our institution (n
¼
12).
PTA was calculated using air conduction lines. Other etiologies of
SSD in the data set include Me´nie`re’s, chronic otitis media, and
sequela from CPA meningioma resection. SD indicates standard
deviation.
TABLE 2.
Institutional protocol for cochlear implantation in
SSD patients
Pure-tone air and bone conduction thresholds
Imittance measures including tympanometry and acoustic reflexes
and otoacoustic emissions
MRI or CT imaging confirmation of a cochlea and cochlear nerve
and to detect inner ear malformations or evidence of ossification
Speech reception thresholds and speech discrimination where age
appropriate (CNC, HINT)
Adaptive HINT is also done with sound field using CROS
amplification and/or the BAHA soft band
Localization testing using a manufacturer-specific ‘‘direct connect’’
system
Vertigo and tinnitus questionnaires are included in the evaluation
All postimplantation testing is performed using a manufacturer-
specific direct connect system
Institutional protocol for cochlear implantation in SSD patients.
SINGLE-SIDED DEAFNESS COCHLEAR IMPLANTATION
Otology & Neurotology, Vol. 37, No. 2, 2016
126