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Inherited Disease
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Retinitis Pigmentosa (RP)
is a hereditary, progressive retinal degeneration in both eyes. Night blindness, usu-
ally in childhood, is followed by loss of peripheral vision (initially as ring-shaped de-
fect). It progresses over many years to tunnel vision and then blindness.
Patchy hypoautofluorescent findings
seen in the periphery in RP
A hyperautofluorescent ring around
the macula can be associated with
central vision loss
Disease activity not easily
visualized on color