315 / 1498
Characteristics (3)
• Prognosis:
– Early stage:
highly curable
– Advanced stage:
multiply relapsing
– Transformation
to HG-NHL particularly TCR-DLBCL
• 10 y risk 10-12%
• 20 y risk up to 30%
• Risk fs: advanced stage, spleen / abdominal presentation
– Importance of
Bx
of every relapse + long FU
– Death
due to NLP is uncommon