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Staging System for Wilms Tumor

I Tumor confined to kidney and completely resected. No

penetration of the renal capsule or involvement of renal

sinus vessels

II Tumor extends beyond kidney but completely resected. (a)

penetration of renal capsule (b) invasion of renal sinus

vessels

III Gross or microscopic residual remains postoperatively

(inoperable tumor, positive surgical margins, tumor spillage

either before or during surgery, regional lymph node

metastases, tumor is removed greater than one piece,

penetration through peritoneal surface)

IV Hematogenous or lymph node metastases outside abdomen

V Bilateral Wilms’ tumor at onset