Primary CNS Lymphoma:
A unique lymphoma entity
•
Increasing incidence
(immunocompetent, older)
•
PCNSL- Confined to brain (occasionally to eyes and CSF)
•
Systemic spread is very rare
•
Multi-centric in the brain in presentation and in relapse
(unlike
gliomas)
•
Resection is not associated with better outcome
•
May initially improve and even temporarily disappear with
steroids (may mask a diagnosis)
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