Argani P et al. Am J Surg Pathol 2000; 24:4-18
Clear Cell Sarcoma of Kidney
First reported by Kidd in 1970
20 cases each year in the US (4-5%
of all renal tumors)
2:1 M:F ratio
29% lymph node mets at
presentation
Most common site of recurrence is
bone and lung, followed by
abdomen and brain