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Difference in Survival Outcome of Primary Central
Nervous System Lymphoma By Histologic Types
Dai Chihara et al. Blood 2017;130:4137
• SEER data on 4,375 adult (≥18 yrs) patients diagnosed
with PCNSL between 1998- 2014
Pathology
Number
Frequency
DLBCL
3,091
70,7%*
Follicular lymphoma
83
1,9%
Peripheral T-cel lymphoma
64
1,5%
Marginal zone lymphoma
63
1,4%
Burkitt lymphoma
27
0,6%
Small lymphocytic lymphoma
22
0,5%
Hodgkin lymphoma
13
0,3%
Other/unclear
1,012
23,1%
Total
4,375
100,0%
* 92% of those with defined histology